Volume 26, Issue 130, December 2022

Dental considerations and management of a patient with dandy-walker syndrome: A case report

Atheer Almulayfi¹, Jawza Alfarraj², Jawaher Alharbi³, Sliuman Alnashwan^4♦, Abdul Aziz Alaeefy⁵

¹Senior Registrar Pediatric Dentistry Department, King Saud Medical City, Riyadh, Saudi Arabia
²Senior Registrar Pediatric Dentistry Department, King Fahad Medical City, Riyadh, Saudi Arabia
³Consultant Pediatric Dentist, Chairman of the Pediatric Dentistry Department, King Saud Medical City, Riyadh, Saudi Arabia
⁴Doctor of Dental Medicine, College of Dentistry, King Saud bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia
⁵General Pediatrics Resident, King Fahad Medical City, Riyadh, Saudi Arabia

^♦Corresponding author
Doctor of Dental Medicine, College of Dentistry, King Saud bin Abdulaziz University for Health Sciences, Riyadh, Saudi Arabia

ABSTRACT

Introduction: Dandy-Walker syndrome is a congenital disorder that mainly affects brain development during pregnancy, particularly the cerebellum, which is the part responsible for movement. An enlargement in the fourth ventricle and cyst formation occurs in this disorder. As cerebrospinal fluid accumulates, high pressure and swelling may occur in the base of the skull causing hydrocephalus. Objective: The purpose of this article is to describe the clinical manifestations, dental considerations, oral findings and management strategies in a DWS-affected pediatric patient. Case description: 4 years old Saudi male patient came with his father with a complaint of multiple caries. The patient was completely uncooperative and refused to sit on the dental chair for examination. The patient was diagnosed with Dandy-Walker syndrome and presented to the clinic with difficulty in swallowing and chronic carious lesions. The swallowing problem is being directed to the swallowing unit at the speech and language pathology department. Under general anesthesia, the patient will go for full dental rehabilitation. Conclusion: Children with Dandy walker syndrome are presented with different clinical presentations and varied intellectual development. The dental management of such children should be costumed for each individual based on their needs. Oral health education for parents and caregivers regarding oral hygiene and dental trauma is of prime importance.

Keywords: Dandy-Walker Syndrome, Hydrocephalus, General Anesthesia, Full Dental Rehabilitation, Pediatrics, Case Report

Medical Science, 2022, 26, ms531e2582

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DOI: https://doi.org/10.54905/disssi/v26i130/ms531e2582

Published: 14 December 2022