Epidermal nevus is a noncancerous growth that causes severe deformities by causing epidermal and adnexal tissue development. Germline mutations in the FGFR3 gene are thought to cause epidermal nevus. Dermatologists are often consulted for treatment in the identification of the lesion based on its clinical appearance. Based on the patient’s situation the doctor must select any one of the best treatment options. This case involves the surgical removal of epidermal nevi in the EAC by an ENT professional. Patients with ILVEN seek medical therapy for both pain alleviation and aesthetic concerns because of the disease's severe and unrelenting symptomatology. Topical medicines, dermabrasion, cryotherapy, laser treatment, and partial-thickness excision have all been investigated. Unfortunately, no one therapy has consistently been found to be effective. Medical therapy is usually unsatisfactory since results are often transient. Surgical therapies have been demonstrated to be more beneficial in terms of symptom reduction, but they come with a significant risk of scarring and recurrence.
Keywords: Epidermal nevus, Topical medicines, dermabrasion, cryotherapy,
laser treatment, and Partial-thickness excision