Swyer James Macleod syndrome (SJMS) is a seldom reported manifestation of post infectious obliterative bronchiolitis in childhood. This cause obliteration of peripheral airways and vascularity of the infected lung and impede lung development. We report SJMS in 31 year old male who presented with complaints of exertional dyspnea, productive cough and hemoptysis and history of recurrent childhood respiratory infections. He had hypoplasia of right lung and right pulmonary vasculature with bronchiectasis as per CT pulmonary angiography while ventilation perfusion scan showed matched V/Q defect diagnosed as SJMS.
Keywords: Pulmonary artery hypoplasia, Swyer James Macleod syndrome,
matched V/Q defect.