A forty year old female presented with weakness of all the four limbs since two days. On evaluation it was found that she was
hypokalemic which she had for last four months. She was further investigated for persistent hypokalemia. On clinical examination
she was found to have sclerodactyly which prompted to consider the diagnosis of systemic sclerosis. The diagnosis was further
supported by presence of antinuclear antibody and anti Scl 70 antibody. Urinary loss of potassium due to distal renal tubular
acidosis was causing hypokalemia. The patient was managed with potassium supplementation.
Keywords: distal renal tubular acidosis, quadriplegia, urinary loss of potassium, scleroderma